Crystal-storing histiocytosis

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August undefined, 2024

WebCrystal-storing histiocytosis (CSH) is a rare non-neoplastic histiocytic lesion with abnormal accumulation of immunoglobulin (Ig) light chain. CSH is associated with Ig overproduction by B ... WebApr 23, 2024 · Crystal-storing histiocytosis (CSH) is a rare disorder characterized by the accumulation of crystallized deposits in the cytoplasm of histiocytes. The entity has been …

Nishino NANAKO Student Hosei University, Tokyo - ResearchGate

WebNov 4, 2024 · Crystal storing histiocytosis (CSH) is a rare condition where crystals accumulate in the cytoplasm of macrophages and is usually associated with a lymphoplasmacytic neoplasm producing a monoclonal immunoglobulin with kappa light chain. CSH with primary manifestation in the skin is extraordinarily ra … WebApr 22, 2024 · Crystal-storing histiocytosis associated with monoclonal kappa light chain gammopathy. Jean-François Lesesve, Corresponding Author. Jean-François Lesesve ... abnormal inclusions shapes were globular, never elongated, crystals as occasionally previously reported. 2, 5 Some inclusions roughly mimicked the Gasser anomaly seen in … philfarmacia

Generalized crystal-storing histiocytosis associated with …

WebMay 29, 2024 · Crystal-storing histiocytosis (CSH) is a rare lesion characterized by sheets of crystal-laden non-neoplastic histiocytes. Characteristic crystalline inclusions within the cytoplasm of histiocytes were first described by Glaus in 1917 [ 1 ]. The condition is still under-recognized given the rare incidence. WebSep 1, 2013 · Crystal-storing histiocytosis refers to deposition of crystalline immunoglobulin inclusions within the cytoplasm of histiocytes. Nearly all patients have underlying neoplasms of plasma cells or B lymphocytes, although occasional patients have no identifiable clonal lymphoplasmacytic disorder. WebA patient who developed a panniculitis with lipid crystallization at the site of etanercept injection is reported on. Panniculitis with lipid crystallization within adipocytes may be seen in several disorders, including crystal‐storing histiocytosis, gouty panniculitis, subcutaneous fat necrosis of the newborn, post‐steroid panniculitis, sclerema … phil farley st petersburg

Crystal-storing histiocytosis as a cause of symptomatic

WebAug 30, 2024 · Crystal-storing histiocytosis is a rare disorder that is morphologically characterized by the accumulation of monoclonal immunoglobulin crystals, … WebJul 31, 2024 · Crystal storing histiocytosis (CSH) is a rare disorder associated with monoclonal gammopathy. It is defined by accumulation of monoclonal heavy and light chains in the lysosome of macrophages. CSH may result in a variety of clinical manifestations depending on the involved organs, but digestive tract involvement is rare. … phil fankhauser columbus ohioWebJul 29, 2024 · CSH is a rare disorder associated with underlying lymphoproliferative or plasma cell disorders. The characteristic morphology should alert the pathologist; … phil fasnacht

"WebThe term crystal-storing histiocytosis should be used when the crystals are noted in the histiocytes and not when the crystals are noted in the epithelial cells of the glomeruli or tubules. Yamamoto et al described a case of crystal-storing histiocytosis in a patient with IgG-κ myeloma. " - Crystal-storing histiocytosis

Crystal-storing histiocytosis

WebNov 1, 2024 · Crystal-storing histiocytosis (CSH) is a rare condition in which crystalline material accumulates in the cytoplasm of histiocytes. Most CSH cases are associated with the expression of monoclonal immunoglobulins (Igs), such as monoclonal gammopathy, multiple myeloma and lymphoplasmacytic lymphoma [ 1 , 2 ]. WebCrystal-storing histiocytosis is a rare diagnosis that to date has only been associated with 2 conditions: intracytoplasmic accumulation of crystallized immunoglobulins in patients with lymphoproliferative disorders or plasma cell dyscrasias, and histiocytic accumulations of phagocytosed clofazimine, a drug used to treat lepromatous leprosy. We describe a 78 …

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WebApr 4, 2024 · Crystal-storing histiocytosis (CSH) is a rare disease associated with the accumulation of histiocytes containing crystalline matter within their cytoplasm. Herein, we present the case of a female patient who was diagnosed with Tolosa–Hunt syndrome at 45 years of age and idiopathic retroperitoneal fibrosis when she was 48 years. She … WebAbstract. Aims: Crystal-storing histiocytosis (CSH) is a rare lesion composed of histiocytes with abnormal intralysosomal accumulation of immunoglobulin (Ig) as …

WebMay 29, 2024 · Crystal-storing histiocytosis (CSH) is a rare lesion characterized by sheets of crystal-laden non-neoplastic histiocytes. Characteristic crystalline inclusions … WebCrystal-storing histiocytosis is a rare disease characterized by the proliferation of non-neoplastic histiocytes that contain crystallized immunoglobulin deposits. It is typically associated with disorders that …

WebFeb 1, 2011 · When previously reported, CSH was seen in the setting of abnormal expression of monoclonal immunoglobulins. 1 These apparent intralysosomal …

WebCrystal-storing histiocytosis: Gaucher disease * Some of the disorders listed here may be associated with the presence of an underlying lymphoproliferative disorder. Graphic 70820 Version 4.0. Company. About Us Editorial Policy …

WebJan 11, 2024 · Crystal-Storing Histiocytosis: The Iceberg of More Serious Conditions 1. Introduction. Crystal-storing histiocytosis is a rare condition that was firstly described … phil farmWebFeb 2, 2024 · Crystal-Storing Histiocytosis; Recent clinical studies. Etiology. Solitary Extramedullary Plasmacytoma of the Lacrimal Sac With Associated Crystal-Storing Histiocytosis. Lee CM, Asilnejad B, Cohen LM, Roelofs KA, Rootman DB, Khanlou N, Pullarkat ST Ophthalmic Plast Reconstr Surg 2024 Mar-Apr 01;38(2):102-107. doi: … phil fay truckeeWebSep 29, 2024 · Crystal-storing histiocytosis is a rare lesion in which crystalline material accumulates in the cytoplasm of histiocytes that are present in soft tissue. phil farrelly bermansWebApr 23, 2024 · Crystal-storing histiocytosis (CSH) is a rare event in disorders associated with monoclonal gammopathy and is mostly associated with the accumulation of immunoglobulins (Igs) in the cytoplasm of histiocytes. In this article, we present a case of a 75-year-old female with IgG kappa monoclonal gammopathy of undetermined … phil fawcett boyleWebSep 1, 2002 · Crystal-storing histiocytosis (CSH) is a rare event in disorders associated with monoclonal gammopathy. The intracellular crystal formation is almost always accompanied by the expression of κ light chains. However, the exact mechanism for the storage has not been clarified until now. phil faulkner island falls maineWebOct 20, 2024 · Crystal-storing histiocytosis (CSH) is an uncommon condition in which histiocytes accumulate a crystalline matter within their cytoplasm. Generally, those crystals are composed of either monoclonal or polyclonal immunoglobulin chains, which have a strong association with an underlying lymphoproliferative or plasma cell disorder (LP-PCD). phil farmer realtor scWebMay 1, 1991 · Crystal-storing histiocytosis has since been reported throughout the body, including lymphoreticular sites (spleen, bone marrow, lymph nodes, and thymus), soft tissues (retroperitoneum, breast,... phil fawell csiro